Basilar impression complicating osteogenesis imperfecta type IV: the clinical and neuroradiological findings in four cases
نویسندگان
چکیده
منابع مشابه
Basilar impression complicating osteogenesis imperfecta type IV: the clinical and neuroradiological findings in four cases.
OBJECTIVES To describe the clinical and neuroradiological features of basilar impression in patients with osteogenesis imperfecta type IV. METHODS Four patients with basilar impression were ascertained in a population study of osteogenesis imperfecta. All four had detailed clinical and neuroradiological examination with both CT and MRI of the craniocervical junction and posterior fossa struct...
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Basilar impression is a well-recognised though rare complication of osteogenesis imperfecta. Three patients, all members of the same family, with advanced basilar impression complicating osteogenesis imperfecta tarda, are described. The clinical features in these cases illustrate the natural history of this condition: from asymptomatic ventricular dilatation, through the foramen magnum compress...
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ژورنال
عنوان ژورنال: Journal of Neurology, Neurosurgery & Psychiatry
سال: 1999
ISSN: 0022-3050
DOI: 10.1136/jnnp.66.3.357